Figure 5From: Eculizumab in paroxysmal nocturnal hemoglobinuria with Budd-Chiari syndrome progressing despite anticoagulation Contrast-enhanced T 1 -weighted MRI. (A) The axial view shows morphological changes and heterogeneous enhancement typical of BCS. A hypervascular nodule is seen consistent with a regenerative nodule (white arrow). A TIPS also is seen (black arrow). Notice collateral circulation in the abdominal wall. (B) The coronal view shows prominent tortuous vascular structures compatible with cavernomatous transformation of the portal vein.Back to article page