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Table 1 Immunological parameters

From: Whole exome sequencing reveals a novel LRBA mutation and clonal hematopoiesis in a common variable immunodeficiency patient presented with hemophagocytic lymphohistiocytosis

Parameters

Measurement at diagnosis

Measurement after HSCT (4 months)

Normal range

Hemoglobin, g/L

57

110

115–150

Platlet,×109/L

5

133

100–300

Leucocytes, ×109/L

7.5

4.5

4–9

Lymphocytes, ×109/L

0.67

1.8

1.1–3.2

B cells, %

2.8

7.26

5.1–20.3

T cells

95.2

86.74

53.7–80.9

 CD3+CD4+, %

19.9

14.8

19.57–48.02

 CD3+CD8+, %

75.3

71.94

15.8–37.5

 CD4+CD25+FOXP3+,%

0.23

0.49

1.11–2.9

NK cell, %

2.0

6

6.7–30.9

Total T/NK lymphocyte, %

8.96

16.94

17.06–43.35

Cytotoxic T/NK Lymphocyte,%

2.29

3.73

2.86–18.22

Non-Cytotoxic T/NK Lymphocyte,%

6.68

13.21

11.15–35.76

IGG, mg/dL

543

1160

860–1740

IGA, mg/dL

10

79

100–420

IGM, mg/dL

18

123

50–280

C3, mg/dL

78

124

70–140

C4, mg/dL

19

36

10–40

sCd25, pg/ml

22914

5367

< 6400

NK cytotoxicity

22.96%

17.44%

≥ 15.11%