1. Beachman et al [5]
|
Diffuse Bullous Amyloidosis of skin
|
Upper Extremities
|
(Am Acad Dermatol)
|
1980
|
Melphalan + Prednisone
|
No Clinical CR, 9 mo
|
2. Ruzicka et al [6]
|
Bullous amyloidosis
|
Generalized Skin
|
(Brit J Dermatol)
|
1985
|
Dapson/Prednisone CR
| |
3. Bieber et al [13]
|
Hemorrhagic Bullous Amyloidosis
|
Multiple skin folds
|
(Arc Dermatol)
|
1988
|
Melphalane + Prednisone
|
Lesions healed with milia
|
4. Johnson et al [2]
|
Non-Hemorrhagic Bullous Amyloidosis
|
Trunk & Proximal Extremities
|
(CUTIS)
|
1989
|
Prednisone + Azathioprine
|
Treatment failed
|
5. Pramatarov et al [14]
|
Multiple Hemorrhagic skin Lesions with systemic Amyloidosis
|
Multiple skin lesions
|
(Intern J Dermatol)
|
1990
|
Cochicine + DMSO
|
Partial response
|
6. Robert et al [3]
|
Bullous Amyloidosis of skin, 3 cases
|
Multiple skin
|
(Medicine)
|
1993
|
Alkylating Agents
|
Poor Response
|
7. Grundmann et al [7]
|
Extensive Hemorrhagic Bollous AA-Amyloidosis
|
Generalized Skin
|
(Eur J. Med)
|
2000
|
Dexamethasone Stabilized after 3 cycles
| |
8. Ochiai et al [15]
|
Bullous Pemphigoid Amyloidosis of Hands Systemic AA-amyloidosis
|
Hands & Feet
|
(J Cutan Pathol)
|
2001
|
CHOP
|
---
|
9. Comenzo et al [16]
|
Review Article Systemic Amyloidosis
|
---
|
(Blood)
|
2002
|
Melphalane + ASCT
|
100-day mortality of 21-39 %
|
10. Gertz et al [17]
|
Primary Systemic Amyloidosis
|
Systemic/Skin
|
(Am J Medicine)
|
2002
|
ASCT
|
Treatment-related Mortality of 14 %
|
11. Goodman et al [18]
|
AL Amyloidosis
|
Systemic/skin
|
(Brit J Haem)
|
2006
|
HD chemotherapy + 100-day mortality ASCT
|
23 %
|
12. Giovanni et al [12]
|
Advanced AL
|
Systemic/Skin Amyloidosis
|
(52nd ASH Meeting)
|
2010
|
Lenalidomide + Dexamethasone Mortality 13 %
|
No CR, PHR 41 %,
|