Author | Clinical Syndrome | Skin Involvement | Reference Published | Year | Treatment | Outcomes |
---|---|---|---|---|---|---|
1. Beachman et al [5] | Diffuse Bullous Amyloidosis of skin | Upper Extremities | (Am Acad Dermatol) | 1980 | Melphalan + Prednisone | No Clinical CR, 9 mo |
2. Ruzicka et al [6] | Bullous amyloidosis | Generalized Skin | (Brit J Dermatol) | 1985 | Dapson/Prednisone CR | Â |
3. Bieber et al [13] | Hemorrhagic Bullous Amyloidosis | Multiple skin folds | (Arc Dermatol) | 1988 | Melphalane + Prednisone | Lesions healed with milia |
4. Johnson et al [2] | Non-Hemorrhagic Bullous Amyloidosis | Trunk & Proximal Extremities | (CUTIS) | 1989 | Prednisone + Azathioprine | Treatment failed |
5. Pramatarov et al [14] | Multiple Hemorrhagic skin Lesions with systemic Amyloidosis | Multiple skin lesions | (Intern J Dermatol) | 1990 | Cochicine + DMSO | Partial response |
6. Robert et al [3] | Bullous Amyloidosis of skin, 3 cases | Multiple skin | (Medicine) | 1993 | Alkylating Agents | Poor Response |
7. Grundmann et al [7] | Extensive Hemorrhagic Bollous AA-Amyloidosis | Generalized Skin | (Eur J. Med) | 2000 | Dexamethasone Stabilized after 3 cycles | Â |
8. Ochiai et al [15] | Bullous Pemphigoid Amyloidosis of Hands Systemic AA-amyloidosis | Hands & Feet | (J Cutan Pathol) | 2001 | CHOP | --- |
9. Comenzo et al [16] | Review Article Systemic Amyloidosis | --- | (Blood) | 2002 | Melphalane + ASCT | 100-day mortality of 21-39 % |
10. Gertz et al [17] | Primary Systemic Amyloidosis | Systemic/Skin | (Am J Medicine) | 2002 | ASCT | Treatment-related Mortality of 14 % |
11. Goodman et al [18] | AL Amyloidosis | Systemic/skin | (Brit J Haem) | 2006 | HD chemotherapy + 100-day mortality ASCT | 23 % |
12. Giovanni et al [12] | Advanced AL | Systemic/Skin Amyloidosis | (52nd ASH Meeting) | 2010 | Lenalidomide + Dexamethasone Mortality 13 % | No CR, PHR 41 %, |